Inherited factor H deficiency and collagen type III glomerulopathy
BA Vogt, RJ Wyatt, BA Burke, SC Simonton… - Pediatric …, 1995 - Springer
BA Vogt, RJ Wyatt, BA Burke, SC Simonton, CE Kashtan
Pediatric Nephrology, 1995•SpringerA non-immune complex-mediated glomerulonephritis associated with persistent
hypocomplementemia occurred in a young boy. Measurement of complement components
revealed complete factor H deficiency, inherited as an autosomal recessive trait. Evaluation
of the renal lesion revealed extensive deposition of type III collagen suggestive of collagen
type III glomerulopathy, a recently identified cause of chronic renal insufficiency in children
and adults. This report represents the first association of inherited factor H deficiency with …
hypocomplementemia occurred in a young boy. Measurement of complement components
revealed complete factor H deficiency, inherited as an autosomal recessive trait. Evaluation
of the renal lesion revealed extensive deposition of type III collagen suggestive of collagen
type III glomerulopathy, a recently identified cause of chronic renal insufficiency in children
and adults. This report represents the first association of inherited factor H deficiency with …
Abstract
A non-immune complex-mediated glomerulonephritis associated with persistent hypocomplementemia occurred in a young boy. Measurement of complement components revealed complete factor H deficiency, inherited as an autosomal recessive trait. Evaluation of the renal lesion revealed extensive deposition of type III collagen suggestive of collagen type III glomerulopathy, a recently identified cause of chronic renal insufficiency in children and adults. This report represents the first association of inherited factor H deficiency with collagen type III glomerulopathy.
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